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Archive ouverte | Zajac, Miroslaw | CCSD

International audience. Introduction: Cystic fibrosis (CF) is caused by defective Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) proteins. CFTR controls chloride (Cl − ) and bicarbonate (HCO 3 − ) transp...

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Archive ouverte | Scudieri, Paolo | CCSD

International audience. Proton secretion mediated by ATP12A protein on the surface of the airway epithelium may contribute to cystic fibrosis (CF) lung disease by favoring bacterial infection and airway obstruction....

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Archive ouverte | Simonin, Juliette | CCSD

International audience

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