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Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis

Archive ouverte | Simonin, Juliette | CCSD

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Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis

Archive ouverte | Simonin, Juliette | CCSD

International audience. Cystic fibrosis (CF) is caused by defective Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) protein. Morbidity is mainly due to early airway infection. We hypothesized that S. aure...

Correction of CFTR function in nasal epithelial cells from cystic fibrosis patients predicts improvement of respiratory function by CFTR modulators

Archive ouverte | Pranke, Iwona | CCSD

International audience

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