Afficher la couverture 'Tolerance of bradykinin-releasing drugs in patients with acquired C1 inhibitor deficiency: a case series and review of the literature. | Escure, Guillaume' en grand format
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Tolerance of bradykinin-releasing drugs in patients with acquired C1 inhibitor deficiency: a case series and review of the literature.

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Escure, Guillaume | Nudel, Morgane | Terriou, Louis | Farhat, Meryem-Maud | Launay, David | Staumont, Delphine | Hachulla, Eric | Gautier, Sophie | Sanges, Sébastien

Edité par CCSD ; John Libbey Eurotext -

International audience. Bradykinin-mediated angioedema (AE) manifests as recurrent oedema of the mucosa, skin and abdominal wall, usually lasting 48 to 96 hours. It can be caused by bradykinin-releasing drugs (such as angiotensin converting enzyme inhibitors [ACEi], angiotensin receptor blockers [ARB] and dipeptidyl peptidase 4 inhibitors [DPP-4i]) or by C1-inhibitor (C1-INH) deficiency, which can be hereditary (HAE) or more rarely acquired (AAE). AAE is classically associated with lymphoid malignancies or monoclonal gammopathy [...]

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