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Portal vein leiomyosarcoma A rare case of hepatic hilar tumor with review of the literature

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Gaignard, Elodie | Bergeat, Damien | Stock, Nathalie | Robin, Fabien | Boudjema, Karim | Sulpice, Laurent | Rayar, Michel | Meunier, B.

Edité par CCSD ; Medknow Publications -

International audience. Portal vein leiomyosarcoma (LMS) is a very rare entity with poor prognosis. Only few cases have been reported in the literature. We report the case of a 53-year-old man with portal vein LMS presenting as a hilar tumor and causing cholestasis. The tumor measured 10 cm and was responsible for right portal vein thrombosis and compression of the biliary convergence. A right hepatectomy with hilar en bloc resection was performed with portal vein and biliary reconstruction. Pathology confirmed the complete resection of a well-differentiated leiomyosarcoma of the portal vein. The postoperative outcome was uneventful and the patient received no adjuvant treatment. Six months after the procedure, the patient is doing well with a normal quality of life and without any sign of recurrence. Aggressive and radical surgery should be proposed in first intention for the treatment of portal vein LMS.

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